Assessment & Research

Temperament in velocardiofacial syndrome.

Antshel et al. (2007) · Journal of intellectual disability research : JIDR 2007
★ The Verdict

VCFS brings slightly tougher temperament traits—check parent-child style fit first when behaviors flare.

✓ Read this if BCBAs serving school-age VCFS learners in clinic or school.
✗ Skip if Practitioners who only treat autism or adults.

01Research in Context

01

What this study did

The team asked parents to fill out the Carey Temperament Scales. They compared kids with velocardiofacial syndrome (VCFS) to same-age peers without the deletion.

All children were 8-14 years old. The study looked at nine temperament traits and at how well parent and child styles matched.

02

What they found

Kids with VCFS scored a little higher on difficult traits. They were more irregular, distractible, and rigid than peers.

When parent and child temperaments clashed, behavior problems jumped. The mismatch predicted symptoms better than VCFS alone.

03

How this fits with other research

Merrill (2004) first mapped the wide VCFS behavioral picture: high ADHD, social withdrawal, language delays, later schizophrenia risk. Plant et al. (2007) zoom in, showing these issues may start with small but stubborn temperament differences.

Lecavalier et al. (2006) used the same Carey scales in autism. Both groups show more extreme scores than typical kids, hinting that routine-loving, distractible profiles cross diagnostic lines.

Furniss et al. (2011) later added cognitive data: verbal strength plus visuospatial and executive holes. Together the papers sketch a full profile—temperament, cognition, and psychiatry—so you know what to watch for at each step.

04

Why it matters

When a learner with VCFS melts down, check temperament fit before adding new rewards. A slow-to-adapt child paired with a go-go parent may need longer warnings, visual schedules, and parent coaching. Matching style to child can cut problem behavior without extra medication.

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→ Action — try this Monday

Give the parent a 5-item Carey quick-screener; if styles clash, add extra transition cues and model calm flexibility during your session.

02At a glance

Intervention
not applicable
Design
quasi experimental
Sample size
67
Population
other
Finding
negative
Magnitude
small

03Original abstract

BACKGROUND: Velocardiofacial syndrome (VCFS) is a microdeletion syndrome caused by a 22q11.2 chromosomal deletion. METHODS: In this study, parents reported on their own temperament as well as the temperament of their child. Sixty-seven children with VCFS (mean age = 10.8, SD = 2.8; range 6-15), and age-, race- and gender-ratio matched samples of 47 community control participants (mean age = 10.4, SD = 2.6; range 6-15), and 18 sibling control participants (mean age = 12.1, SD = 1.9; range 9-15) took part in the current project. RESULTS: Children with VCFS have a temperament that may best be described as modestly difficult; while participants with VCFS were not more difficult across all temperamental domains, children with VCFS were rated by their parents as being: (1) less regular in their daily habits (e.g. eating at the same time each day, etc.); (2) less able to focus/sustain attention; (3) less cheerful/pleasant; (4) less likely to stay with an activity for a long time; and (5) less able to respond flexibly to changes in the environment. CONCLUSIONS: The best predictors of parent report of behavioural symptoms in children with VCFS were poor concordance between parent and child temperament across general activity level and mood domains.

Journal of intellectual disability research : JIDR, 2007 · doi:10.1111/j.1365-2788.2006.00859.x