Brief Report: Contrasting Profiles of Everyday Executive Functioning in Smith-Magenis Syndrome and Down Syndrome.
Use the BRIEF-P to spot wider everyday executive-function gaps in preschoolers with Smith-Magenis versus Down syndrome.
01Research in Context
What this study did
Wilde et al. (2017) asked caregivers of preschoolers to fill out the BRIEF-P. The form lists everyday executive-function skills like planning and self-control.
The team compared two groups: children with Smith-Magenis syndrome and children with Down syndrome. They wanted to see which group showed wider EF problems.
What they found
Caregivers ticked more problem items for the Smith-Magenis group. The Down group looked milder on every-day EF.
The wider EF gaps in Smith-Magenis line up with its higher risk for behavior disorders.
How this fits with other research
Austin et al. (2015) already showed the BRIEF-P works in Down syndrome kids. Wilde et al. (2017) built on that by using the same tool to contrast two syndromes.
Miezah et al. (2026) later ran the same kind of check in adults with Down syndrome. Together the three papers trace an EF picture from preschool to adulthood in Down syndrome.
Wilde et al. (2013) used the same two-syndrome design but looked at social attention. Pairing the 2013 and 2017 papers gives you both social and EF maps for the same kids.
Why it matters
If you assess a child with Smith-Magenis, expect broad EF weak spots and plan extra supports for working memory and shifting. For Down syndrome, expect fewer daily EF issues in preschool yet still screen each domain; later studies show problems can grow with age. Add the BRIEF-P to your intake packet for both groups and re-check at yearly updates.
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02At a glance
03Original abstract
Everyday executive function (EF) was examined in Smith-Magenis syndrome (SMS), associated with high risk of behaviour disorder, and Down syndrome (DS), associated with relatively low risk of behaviour disorder. Caregivers of 13 children with SMS and 17 with DS rated everyday EF using the Behavioral Rating Inventory of Executive Functioning-Preschool. Greater everyday EF deficits relative to adaptive ability were evident in SMS than in DS. The SMS profile of everyday EF abilities was relatively uniform; in DS emotional control strengths and working memory weaknesses were evident. Findings implicate broad everyday EF difficulties in SMS compared to DS, corresponding with increased rates of behaviour disorder in SMS. Findings further suggest that everyday EF profiles may, in part, be syndrome related.
Journal of autism and developmental disorders, 2017 · doi:10.1007/s10803-017-3140-2