Assessment & Research

Visuo-spatial and linguistic abilities in a twin with Williams syndrome.

Volterra et al. (1999) · Journal of intellectual disability research : JIDR 1999
★ The Verdict

Williams syndrome brings broad delay yet keeps sharp face naming and word fluency, so test and teach these strengths while watching for slower processing speed.

✓ Read this if BCBAs assessing or writing programs for school-age kids with Williams syndrome.
✗ Skip if Clinicians only serving adults with WS or teams focused on severe problem behavior.

01Research in Context

01

What this study did

Doctors compared one twin with Williams syndrome to her sister without it. They gave both girls the same tests for space skills, words, and memory. The goal was to see which skills stayed strong and which lagged behind.

02

What they found

The Williams twin showed broad delays, yet she beat her sister on three tasks. She named more faces, listed more words that start with 'S', and recalled specific stories better. These pockets of strength sat inside an overall slow profile.

03

How this fits with other research

Amore et al. (2011) later tested face attention in a bigger WS group. They found the same long face gaze, but showed it comes from slow disengagement, not super-powered recognition. The twin data and the group data line up: faces hold WS attention longer.

Emerson et al. (2007) added emotional faces and upside-down faces. WS kids again outscored autism peers on upright happy or angry faces, yet fell apart when faces flipped. Together the papers say: expect face skill only when photos are upright and emotional.

Hsu (2013) looked at picture context, not faces. WS people could still combine scene clues like controls, just slower. So the 'islands of strength' idea keeps showing up, but speed is the hidden cost.

04

Why it matters

When you test a child with Williams syndrome, probe face naming and verbal fluency first. These quick wins build rapport and show caregivers what is possible. Keep tasks short, because even spared skills run on a slower clock. Use upright, expressive photos for social training; skip inverted or neutral images that trip them up. Finally, share the twin story with parents: delays are real, but bright spots are measurable and teachable.

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Open your next WS session with a 1-minute 'name that face' game using upright, smiling photos to boost engagement and collect easy baseline data.

02At a glance

Intervention
not applicable
Design
case study
Sample size
2
Population
other
Finding
not reported

03Original abstract

The present study reports a case of dizygotic twins, one boy with Williams syndrome (WS) and one typically developing girl, and compares their neuropsychological profiles. The goal of the present authors was to verify whether the child with WS displayed a cognitive profile which is unique to the syndrome. Several tests designed to assess visuo-perceptual, visuo-motor, linguistic and memory abilities were administered to both children when they were 10.9 years old. Compared to his sister, the boy with WS displayed a homogeneous developmental delay in both non-verbal and verbal abilities. He achieved a level of performance similar to his sister only in facial recognition, phonological word fluency and memory for phonologically similar words. Furthermore, despite the overall delayed performance of the boy, both the twins displayed a cognitive profile characterized by strength in lexical comprehension and relative weakness in visuo-motor abilities.

Journal of intellectual disability research : JIDR, 1999 · doi:10.1046/j.1365-2788.1999.00216.x